PASTORE, Nunzia
PASTORE, Nunzia
DIPARTIMENTO DI SCIENZE MEDICHE TRASLAZIONALI
Correction of hyperbilirubinemia in Gunn rats by surgical delivery of low doses of HDAd vectors.
2014 Schmitt, F; Pastore, N; Abarrategui Pontes, C; Flageul, M; Myara, A; Laplanche, S; Labrune, P; Podevin, G; Nguyen, T; BRUNETTI PIERRI, Nicola
Sustained Reduction of Hyperbilirubinemia in Gunn Rats after Adeno-Associated Virus-Mediated Gene Transfer of Bilirubin UDP-Glucuronosyltransferase Isozyme 1A1 to Skeletal Muscle.
2012 Pastore, N; Nusco, E; Vaníkova, J; Sepe, Rm; Vetrini, F; Mcdonagh, A; Auricchio, Alberto; Vitek, L; BRUNETTI PIERRI, Nicola
Autophagy master regulator TFEB induces clearance of toxic SERPINA1/?-1-antitrypsin polymers.
2013 Pastore, N; Ballabio, Andrea; BRUNETTI PIERRI, Nicola
Improved efficacy and reduced toxicity by ultrasound-guided intrahepatic injections of helper-dependent adenoviral vector in Gunn rats.
2013 Pastore, N; Nusco, E; Piccolo, P; Castaldo, S; Van?kova, J; Vetrini, F; Palmer, Dj; Vitek, L; Ng, P; BRUNETTI PIERRI, Nicola
Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy
2015 Hidvegi, Tunda; Stolz, Donna B; Alcorn, John F; Yousem, Samuel A; Wang, Jieru; Leme, Adriana S; Houghton, A. McGarry; Hale, Pamela; Ewing, Michael; Cai, Houming; Garchar, Evelyn Akpadock; Pastore, Nunzia; Annunziata, Patrizia; Kaminski, Naftali; Pilewski, Joseph; Shapiro, Steven D; Pak, Stephen C; Silverman, Gary A; BRUNETTI PIERRI, Nicola; Perlmutter, David H.
TFEB and TFE3 Cooperate in the Regulation of the Innate Immune Response in Activated Macrophages
2016 Pastore, Nunzia; Brady, Owen A; Diab, Heba I; Martina, José A; Sun, Lu; Huynh, Tuong; Lim, Jeong A; Zare, Hossein; Raben, Nina; Ballabio, Andrea; Puertollano, Rosa
TFE3 regulates whole-body energy metabolism in cooperation with TFEB
2017 Pastore, Nunzia; Vainshtein, Anna; Klisch, Tiemo J; Armani, Andrea; Huynh, Tuong; Herz, Niculin J; Polishchuk, Elena V; Sandri, Marco; Ballabio, Andrea
Transcriptional activation of RagD GTPase controls mTORC1 and promotes cancer growth
2017 DI MALTA, Chiara; Siciliano, Diletta; Calcagni, Alessia; Monfregola, Jlenia; Punzi, Simona; Pastore, Nunzia; Eastes, Andrea N; Davis, Oliver; De Cegli, Rossella; Zampelli, Angela; Di Giovannantonio, Luca G; Nusco, Edoardo; Platt, Nick; Guida, Alessandro; Ogmundsdottir, Margret Helga; Lanfrancone, Luisa; Perera, Rushika M; Zoncu, Roberto; Pelicci, Pier Giuseppe; Settembre, Carmine; Ballabio, Andrea
Activation of JNK pathway aggravates proteotoxicity of hepatic mutant Z alpha1-antitrypsin
2017 Pastore, Nunzia; Attanasio, Sergio; Granese, Barbara; Teckman, Jeffrey; Wilson, Andrew A; Ballabio, Andrea; BRUNETTI PIERRI, Nicola
Enhancement of hepatic autophagy increases ureagenesis and protects against hyperammonemia
2017 Soria, Leandro R.; Allegri, Gabriella; Melck, Dominique; Pastore, Nunzia; Annunziata, Patrizia; Paris, Debora; Polishchuk, Elena; Nusco, Edoardo; Thöny, Beat; Motta, Andrea; Häberle, Johannes; Ballabio, Andrea; Brunetti-Pierri, Nicola
Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha-1- anti-trypsin deficiency.
2013 Pastore, N.; Blomenkamp, K.; Annunziata, Fabio; Piccolo, P.; Mithbaokar, P.; Sepe, R. M.; Vetrini, F.; Palmer, D.; Ng, P.; Polishchuk, P.; Iacobacci, S.; Polishchuk, R.; Teckman, J.; Ballabio, A.; BRUNETTI PIERRI, Nicola
Fasting Imparts a Switch to Alternative Daily Pathways in Liver and Muscle
2018 Kinouchi, Kenichiro; Magnan, Christophe; Ceglia, Nicholas; Liu, Yu; Cervantes, Marlene; Pastore, Nunzia; Huynh, Tuong; Ballabio, Andrea; Baldi, Pierre; Masri, Selma; Sassone-Corsi, Paolo
Wilson disease protein ATP7B utilizes lysosomal exocytosis to maintain copper homeostasis
2014 Polishchuk, Ev; Concilli, M; Iacobacci, S; Chesi, G; Pastore, N; Piccolo, P; Paladino, S; Baldantoni, D; van IJzendoorn, Sc; Chan, J; Chang, Cj; Amoresano, A.; Pane, F; Pucci, P; Tarallo, A; Parenti, Giancarlo; Brunetti Pierri, N; Settembre, Carmine; Ballabio, Andrea; Polishchuk, Rs; Pucci, Pietro
Nutrient-sensitive transcription factors TFEB and TFE3 couple autophagy and metabolism to the peripheral clock
2019 Pastore, N.; Vainshtein, A.; Herz, N. J.; Huynh, T.; Brunetti, L.; Klisch, T. J.; Mutarelli, M.; Annunziata, P.; Kinouchi, K.; Brunetti-Pierri, N.; Sassone-Corsi, P.; Ballabio, A.
Keeping the autophagy tempo
2019 Pastore, Nunzia; Ballabio, Andrea
TFEB gene therapy of alpha-1-antitrypsin deficiency”
2012 Ballabio, A; BRUNETTI PIERRI, Nicola; Pastore, N
Reply
2017 Pastore, Nunzia; Attanasio, Sergio; BRUNETTI PIERRI, Nicola
Potentiation of rifampin activity in a mouse model of tuberculosis by activation of host transcription factor EB
2020 Bryk, R.; Mundhra, S.; Jiang, X.; Wood, M.; Pfau, D.; Weber, E.; Park, S.; Zhang, L.; Wilson, C.; Van der Westhuyzen, R.; Street, L.; Chibale, K.; Zimmerman, M.; Dartois, V.; Pastore, N.; Ballabio, A.; Hawryluk, N.; Canan, S.; Khetani, V.; Camardo, J.; Nathan, C.
TFEB regulates murine liver cell fate during development and regeneration
2020 Pastore, N.; Huynh, T.; Herz, N. J.; Calcagni', A.; Klisch, T. J.; Brunetti, L.; Kim, K. H.; De Giorgi, M.; Hurley, A.; Carissimo, A.; Mutarelli, M.; Aleksieva, N.; D'Orsi, L.; Lagor, W. R.; Moore, D. D.; Settembre, C.; Finegold, M. J.; Forbes, S. J.; Ballabio, A.
HDAC6-dependent ciliophagy is involved in ciliary loss and cholangiocarcinoma growth in human cells and murine models
2020 Peixoto, E.; Jin, S.; Thelen, K.; Biswas, A.; Richard, S.; Morleo, M.; Mansini, A.; Holtorf, S.; Carbone, F.; Pastore, N.; Ballabio, A.; Franco, B.; Gradilone, S. A.
Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
---|---|---|---|---|
Correction of hyperbilirubinemia in Gunn rats by surgical delivery of low doses of HDAd vectors. | 1.1 Articolo in rivista | 2014 | Schmitt, F; Pastore, N; Abarrategui Pontes, C; Flageul, M; Myara, A; Laplanche, S; Labrune, P; Podevin, G; Nguyen, T; BRUNETTI PIERRI, Nicola | |
Sustained Reduction of Hyperbilirubinemia in Gunn Rats after Adeno-Associated Virus-Mediated Gene Transfer of Bilirubin UDP-Glucuronosyltransferase Isozyme 1A1 to Skeletal Muscle. | 1.1 Articolo in rivista | 2012 | Pastore, N; Nusco, E; Vaníkova, J; Sepe, Rm; Vetrini, F; Mcdonagh, A; Auricchio, Alberto; Vitek, L; BRUNETTI PIERRI, Nicola | |
Autophagy master regulator TFEB induces clearance of toxic SERPINA1/?-1-antitrypsin polymers. | 1.1 Articolo in rivista | 2013 | Pastore, N; Ballabio, Andrea; BRUNETTI PIERRI, Nicola | |
Improved efficacy and reduced toxicity by ultrasound-guided intrahepatic injections of helper-dependent adenoviral vector in Gunn rats. | 1.1 Articolo in rivista | 2013 | Pastore, N; Nusco, E; Piccolo, P; Castaldo, S; Van?kova, J; Vetrini, F; Palmer, Dj; Vitek, L; Ng, P; BRUNETTI PIERRI, Nicola | |
Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy | 1.1 Articolo in rivista | 2015 | Hidvegi, Tunda; Stolz, Donna B; Alcorn, John F; Yousem, Samuel A; Wang, Jieru; Leme, Adriana S; Houghton, A. McGarry; Hale, Pamela; Ewing, Michael; Cai, Houming; Garchar, Evelyn Akpadock; Pastore, Nunzia; Annunziata, Patrizia; Kaminski, Naftali; Pilewski, Joseph; Shapiro, Steven D; Pak, Stephen C; Silverman, Gary A; BRUNETTI PIERRI, Nicola; Perlmutter, David H. | |
TFEB and TFE3 Cooperate in the Regulation of the Innate Immune Response in Activated Macrophages | 1.1 Articolo in rivista | 2016 | Pastore, Nunzia; Brady, Owen A; Diab, Heba I; Martina, José A; Sun, Lu; Huynh, Tuong; Lim, Jeong A; Zare, Hossein; Raben, Nina; Ballabio, Andrea; Puertollano, Rosa | |
TFE3 regulates whole-body energy metabolism in cooperation with TFEB | 1.1 Articolo in rivista | 2017 | Pastore, Nunzia; Vainshtein, Anna; Klisch, Tiemo J; Armani, Andrea; Huynh, Tuong; Herz, Niculin J; Polishchuk, Elena V; Sandri, Marco; Ballabio, Andrea | |
Transcriptional activation of RagD GTPase controls mTORC1 and promotes cancer growth | 1.1 Articolo in rivista | 2017 | DI MALTA, Chiara; Siciliano, Diletta; Calcagni, Alessia; Monfregola, Jlenia; Punzi, Simona; Pastore, Nunzia; Eastes, Andrea N; Davis, Oliver; De Cegli, Rossella; Zampelli, Angela; Di Giovannantonio, Luca G; Nusco, Edoardo; Platt, Nick; Guida, Alessandro; Ogmundsdottir, Margret Helga; Lanfrancone, Luisa; Perera, Rushika M; Zoncu, Roberto; Pelicci, Pier Giuseppe; Settembre, Carmine; Ballabio, Andrea | |
Activation of JNK pathway aggravates proteotoxicity of hepatic mutant Z alpha1-antitrypsin | 1.1 Articolo in rivista | 2017 | Pastore, Nunzia; Attanasio, Sergio; Granese, Barbara; Teckman, Jeffrey; Wilson, Andrew A; Ballabio, Andrea; BRUNETTI PIERRI, Nicola | |
Enhancement of hepatic autophagy increases ureagenesis and protects against hyperammonemia | 1.1 Articolo in rivista | 2017 | Soria, Leandro R.; Allegri, Gabriella; Melck, Dominique; Pastore, Nunzia; Annunziata, Patrizia; Paris, Debora; Polishchuk, Elena; Nusco, Edoardo; Thöny, Beat; Motta, Andrea; Häberle, Johannes; Ballabio, Andrea; Brunetti-Pierri, Nicola | |
Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha-1- anti-trypsin deficiency. | 1.1 Articolo in rivista | 2013 | Pastore, N.; Blomenkamp, K.; Annunziata, Fabio; Piccolo, P.; Mithbaokar, P.; Sepe, R. M.; Vetrini, F.; Palmer, D.; Ng, P.; Polishchuk, P.; Iacobacci, S.; Polishchuk, R.; Teckman, J.; Ballabio, A.; BRUNETTI PIERRI, Nicola | |
Fasting Imparts a Switch to Alternative Daily Pathways in Liver and Muscle | 1.1 Articolo in rivista | 2018 | Kinouchi, Kenichiro; Magnan, Christophe; Ceglia, Nicholas; Liu, Yu; Cervantes, Marlene; Pastore, Nunzia; Huynh, Tuong; Ballabio, Andrea; Baldi, Pierre; Masri, Selma; Sassone-Corsi, Paolo | |
Wilson disease protein ATP7B utilizes lysosomal exocytosis to maintain copper homeostasis | 1.1 Articolo in rivista | 2014 | Polishchuk, Ev; Concilli, M; Iacobacci, S; Chesi, G; Pastore, N; Piccolo, P; Paladino, S; Baldantoni, D; van IJzendoorn, Sc; Chan, J; Chang, Cj; Amoresano, A.; Pane, F; Pucci, P; Tarallo, A; Parenti, Giancarlo; Brunetti Pierri, N; Settembre, Carmine; Ballabio, Andrea; Polishchuk, Rs; Pucci, Pietro | |
Nutrient-sensitive transcription factors TFEB and TFE3 couple autophagy and metabolism to the peripheral clock | 1.1 Articolo in rivista | 2019 | Pastore, N.; Vainshtein, A.; Herz, N. J.; Huynh, T.; Brunetti, L.; Klisch, T. J.; Mutarelli, M.; Annunziata, P.; Kinouchi, K.; Brunetti-Pierri, N.; Sassone-Corsi, P.; Ballabio, A. | |
Keeping the autophagy tempo | 1.1 Articolo in rivista | 2019 | Pastore, Nunzia; Ballabio, Andrea | |
TFEB gene therapy of alpha-1-antitrypsin deficiency” | 6.1 Brevetto | 2012 | Ballabio, A; BRUNETTI PIERRI, Nicola; Pastore, N | |
Reply | 1.7 Commento, erratum, replica e simili | 2017 | Pastore, Nunzia; Attanasio, Sergio; BRUNETTI PIERRI, Nicola | |
Potentiation of rifampin activity in a mouse model of tuberculosis by activation of host transcription factor EB | 1.1 Articolo in rivista | 2020 | Bryk, R.; Mundhra, S.; Jiang, X.; Wood, M.; Pfau, D.; Weber, E.; Park, S.; Zhang, L.; Wilson, C.; Van der Westhuyzen, R.; Street, L.; Chibale, K.; Zimmerman, M.; Dartois, V.; Pastore, N.; Ballabio, A.; Hawryluk, N.; Canan, S.; Khetani, V.; Camardo, J.; Nathan, C. | |
TFEB regulates murine liver cell fate during development and regeneration | 1.1 Articolo in rivista | 2020 | Pastore, N.; Huynh, T.; Herz, N. J.; Calcagni', A.; Klisch, T. J.; Brunetti, L.; Kim, K. H.; De Giorgi, M.; Hurley, A.; Carissimo, A.; Mutarelli, M.; Aleksieva, N.; D'Orsi, L.; Lagor, W. R.; Moore, D. D.; Settembre, C.; Finegold, M. J.; Forbes, S. J.; Ballabio, A. | |
HDAC6-dependent ciliophagy is involved in ciliary loss and cholangiocarcinoma growth in human cells and murine models | 1.1 Articolo in rivista | 2020 | Peixoto, E.; Jin, S.; Thelen, K.; Biswas, A.; Richard, S.; Morleo, M.; Mansini, A.; Holtorf, S.; Carbone, F.; Pastore, N.; Ballabio, A.; Franco, B.; Gradilone, S. A. |