BALLABIO, ANDREA

BALLABIO, ANDREA  

DIPARTIMENTO DI SCIENZE MEDICHE TRASLAZIONALI  

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Titolo Tipologia Data di pubblicazione Autore(i) File
X-linked recessive chondrodysplasia punctata: spectrum of arylsulfatase E gene mutations and expanded clinical variability 1.1 Articolo in rivista 2003 BRUNETTI PIERRI, Nicola; Andreucci, M. V.; Tuzzi, R.; Vega, G. R.; Gray, G.; Mckeown, C; Ballabio, Andrea; Andria, Generoso; Meroni, G.; Parenti, G.
SLC7A7, encoding a putative permease-related protein, is mutated in patients with lysinuric protein intolerance. 1.1 Articolo in rivista 1999 Borsani, G.; Bassi, Mt; Sperandeo, Mp; DE GRANDI, A.; Buoninconti, A.; Riboni, M.; Manzoni, M.; Incerti, B.; Andria, Generoso; Ballabio, Andrea; Sebastio, G.
Endothelin-B receptor mutations in patients with isolated Hirschsprung disease from a non inbred population. 1.1 Articolo in rivista 1996 Auricchio, Alberto; Casari, G.; Staiano, Annamaria; Ballabio, Andrea
Slc7a7 disruption causes fetal growth retardation by downregulating Igf1 in the mouse model of lysinuric protein intolerance. 1.1 Articolo in rivista 2007 Sperandeo, Mp; Annunziata, P; Bozzato, A; Piccolo, P; Maiuri, L; D'Armiento, M; Ballabio, Andrea; Corso, G; Andria, Generoso; Borsani, G; Sebastio, Gianfranco
Steroid Sulfatase Deficiency and X-linked Ichthyosis. 2.1 Contributo in volume (Capitolo o Saggio) 1995 Ballabio, Andrea; Shapiro, L. J.
Molecular heterogeneity of steroid sulfatase deficiency: a multicenter study on 57 unrelated patients, at DNA and protein levels. 1.1 Articolo in rivista 1989 Ballabio, Andrea; R., Carrozzo; G., Parenti; A., Gil; Zollo, Massimo; M. G., Persico; E., Gillard; N., Affara; J., Yates; M. A., FERGUSON SMITH
Deletion of the distal short arm of the X chromosome (Xp) in a patient with short stature, chondrodysplasia punctata, and X-linked ichthyosis due to steroid sulfatase deficiency 1.1 Articolo in rivista 1991 Ballabio, A; Zollo, Massimo; R., Carrozzo; A., Caiulo; O., Zuffardi; C. F., Cascioli; D., Viggiano; Strisciuglio, Pietro
Screening for steroid sulfatase (STS) gene deletions by multiplex DNA amplification. 1.1 Articolo in rivista 1990 Ballabio, Andrea; Ranier, J. E.; Chamberlain, J. S.; Zollo, Massimo; Caskey, C. T.
Axonal degeneration in paraplegin-deficient mice is associated with abnormal mitochondria and impairment of axonal transport. 1.1 Articolo in rivista 2004 Ferreirinha, F; Quattrini, A; Pirozzi, M; Valsecchi, V; Dina, G; Broccoli, V; Piemonte, F; Tozzi, G; Gaeta, L; Casari, G; Ballabio, Andrea; AND RUGARLI, E. I.
Multiple sulfatase deficiency in a Turkish family resulting from a novel mutation. 1.1 Articolo in rivista 2008 Yiş, U.; Pepe, S.; Kurul, S. H.; Ballabio, Andrea; Cosma, M. P.; Dirik, E.
MicroRNA target prediction by expression analysis of host genes. 1.1 Articolo in rivista 2009 Gennarino, Va; Sardiello, M; Avellino, R; Meola, N; Maselli, V; Anand, S; Cutillo, L; Ballabio, Andrea; Banfi, S.
Deletion of the distal short arm of the X chromosome (Xp) in a patient with short stature, chondrodysplasia punctata, and X-linked ichthyosis due to steroid sulfatase deficiency. 1.1 Articolo in rivista 1991 Ballabio, Andrea; Zollo, Massimo; Carrozzo, R; Caiulo, A; Zuffardi, O; Cascioli, Cf; Viggiano, D; Strisciuglio, Pietro
Lysosomal disorders: From storage to cellular damage 1.1 Articolo in rivista 2009 Ballabio, Andrea; Gieselmann, V.
Lysosomal enhancement: a CLEAR answer to cellular degradative needs 1.1 Articolo in rivista 2009 Sardiello, M.; Ballabio, Andrea
Disease pathogenesis explained by basic science: lysosomal storage diseases as autophagocytic disorders 1.1 Articolo in rivista 2009 Ballabio, Andrea
Lack of sik1 in mouse embryonic stem cells impairs cardiomyogenesis by down-regulating the cyclin-dependent kinase inhibitor p57kip2 1.1 Articolo in rivista 2010 Romito, A; Lonardo, E; Roma, G; Minchiotti, G; Ballabio, Andrea; Cobellis, G.
In vivo doxycycline controlled regulated system in photoreceptor cells. 1.1 Articolo in rivista 2003 Angeletti, B.; Löster, J.; Auricchio, Alberto; Ballabio, Andrea; Graw, J.; Marigo, V.
Identification of incomplete coding sequences for steroid sulphatase on the human Y chromosome: evidence for an ancestral pseudoautosomal gene? 1.1 Articolo in rivista 1987 Fraser, N; Ballabio, Andrea; Zollo, Massimo; Persico, G; Craig, I.
X-linked Alport syndrome: an SSCP-based mutation survey over all 51 exons of the COL4A5 gene. 1.1 Articolo in rivista 1996 Renieri, A; Bruttini, M; Galli, L; Zanelli, P; Neri, T; Rossetti, S; Turco, A; Heiskari, N; Zhou, J; Gusmano, R; Massella, L; Banfi, G; Scolari, F; Sessa, A; Rizzoni, G; Tryggvason, K; Pignatti, P. F.; Savi, M; Ballabio, Andrea; DE MARCHI, M.
Expression pattern of the Tbr-2 (Eomesodermin) gene during mouse and chick brain development. 1.1 Articolo in rivista 1999 Bulfone, A; Martinez, S; Marigo, V; Campanella, M; Basile, A; Quaderi, N; Gattuso, C; Rubenstein, J. L. R.; Ballabio, Andrea