Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.
Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance / Di Dato, F., Spadarella, S., Puoti, M.G., Caprio, M.G., Pagliardini, S., Zuppaldi, C., Vallone, G., Fecarotta, S., Esposito, G., Iorio, R., Parenti, G., Spagnuolo, M.I.. - In: NUTRIENTS. - ISSN 2072-6643. - 11:10(2019). [10.3390/nu11102397]
Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance
Di Dato, Fabiola;Spadarella, Simona;Puoti, Maria Giovanna;Caprio, Maria Grazia;Vallone, Gianfranco;Fecarotta, Simona;Esposito, Gabriella;Iorio, Raffaele;Parenti, Giancarlo
;Spagnuolo, Maria Immacolata
2019
Abstract
Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.


